Page 5 of 8
Kniest dysplasia is a type of chondrodysplasia characterized by severe craniofacial abnormalities including tracheomalacia, midface hypoplasia, and cleft palate.
Citation: JA Clinical Reports 2018 4:41
Perioperative seizure control is correlated with a better surgical outcome for awake craniotomy, but some anticonvulsants can induce hyponatremia. Mannitol has also been reported to be hyponatremic.
Citation: JA Clinical Reports 2018 4:40
Citation: JA Clinical Reports 2018 4:39
Hereditary angioedema is a rare genetic disorder resulting from an inherited deficiency or dysfunction of the C1-esterase inhibitor. In the anesthetic management of such patients, special caution should be exe...
Citation: JA Clinical Reports 2018 4:38
Recessive dystrophic epidermolysis bullosa (RDEB) is a rare, hereditary mucocutaneous disorder that can involve renal insufficiency. If a vascular access for hemodialysis is unavailable, peritoneal dialysis ca...
Citation: JA Clinical Reports 2018 4:37
Hip fracture is a common and serious orthopedic injury among the geriatric population, necessitating surgical treatment. We tested whether age is a significant risk factor for in-hospital mortality after surge...
Citation: JA Clinical Reports 2018 4:36
Pheochromocytoma is a rare catecholamine-secreting tumor. To evaluate the intraoperative hemodynamics with precision is difficult.
Citation: JA Clinical Reports 2018 4:35
We report the case of a child with Krabbe disease who underwent three repeated surgeries and anesthetic management, and we discuss the major concerns about Krabbe disease and the usefulness of a perioperative ...
Citation: JA Clinical Reports 2018 4:34
Citation: JA Clinical Reports 2018 4:33
Rett syndrome, which is a progressive, central nervous system disease that is caused by a gene mutation, is known to present with various symptoms. This case is that of a 15-year-old girl who was diagnosed wit...
Citation: JA Clinical Reports 2018 4:32
Citation: JA Clinical Reports 2018 4:31
Citation: JA Clinical Reports 2018 4:30
Citation: JA Clinical Reports 2018 4:29
Citation: JA Clinical Reports 2018 4:28
Citation: JA Clinical Reports 2018 4:27
Previous case reports suggested that the presence of obstruction in the passage of the pulmonary artery catheter (PAC) may hinder its placement. However, little is known regarding the difficulty in proper plac...
Citation: JA Clinical Reports 2018 4:26
We have reviewed four cases of Kawasaki disease treated with plasma exchange with 5% albumin in electrolyte-balanced solution, according to the recommended guidelines for Kawasaki disease in the intensive care...
Citation: JA Clinical Reports 2018 4:25
We herein report anesthetic management during aortic valve replacement for aortic valve regurgitation in a patient with adult mucopolysaccharidosis type II (MPS type 2) (Hunter syndrome). This disorder is rare...
Citation: JA Clinical Reports 2018 4:24
We report a case of unexpected ventilatory impairment that occurred during per-oral endoscopic myotomy (POEM) under general anesthesia. A 73-year-old woman underwent POEM for Jackhammer esophagus. The patient ...
Citation: JA Clinical Reports 2018 4:23
We encountered a 59-year-old man who first underwent left internal carotid endarterectomy for left internal carotid artery stenosis and then presented with postoperative swelling of the bilateral salivary glan...
Citation: JA Clinical Reports 2018 4:22
Citation: JA Clinical Reports 2018 4:21
The Retraction Note to this article has been published in JA Clinical Reports 2020 6:41
Pallister–Hall syndrome is a rare disorder characterized by hypothalamic hamartoma, hypopituitarism, bifid epiglottis, and micrognathia.
Citation: JA Clinical Reports 2018 4:20
Citation: JA Clinical Reports 2018 4:19
Subdural hematoma (SDH) after accidental dural puncture (ADP) is rare but may be lethal. We experienced a patient who developed SDH after combined spinal and epidural anesthesia without a headache.
Citation: JA Clinical Reports 2018 4:18
Protein S deficiency patient is characterized by recurrent thrombosis, and its risk is higher intraoperatively, especially in cardiac surgery involving cardiopulmonary bypass. Two heparin cessation periods are...
Citation: JA Clinical Reports 2018 4:17
Heterotaxy syndrome (HS) is characterized by a wide variety of cardiac and extra-cardiac malformations, including pulmonary valve stenosis, interruption of the inferior vena cava, total anomalous pulmonary ven...
Citation: JA Clinical Reports 2018 4:16
The placement of a pulmonary artery catheter sometimes needs long time by observing the pressure wave, and several factors have been reported to hinder the placement. In the present study, we examined whether ...
Citation: JA Clinical Reports 2018 4:15
Anti-N-methyl-D-aspartate receptor (NMDAR) encephalitis is an autoimmune disorder caused by production of anti-NMDAR antibodies that is often associated with ovarian teratoma and exhibits various manifestation...
Citation: JA Clinical Reports 2018 4:14
A 64-year-old female patient with spinocerebellar ataxia type 6 was referred to our department for pancreatic cancer and anesthetized with volatile anesthesia combined with epidural anesthesia for pancreaticod...
Citation: JA Clinical Reports 2018 4:13
Progressive supranuclear palsy (PSP) is one of the rare diseases. PSP is characterized by oculomotor dysfunction, postural instability, akinesia, dysarthria, and dysphagia. The major cause of death in patients...
Citation: JA Clinical Reports 2018 4:12
Polymeraze I and transcript release factor (PTRF) mutations are a newly recognized disease, which cause congenital generalized lipodystrophy associated with myopathy.
Citation: JA Clinical Reports 2018 4:11
Serratus plane block is a thoracic truncal block that has been proposed as alternatives for analgesia such as epidural anesthesia and paravertebral block for the anterolateral chest wall. Previously, we perfor...
Citation: JA Clinical Reports 2018 4:10
Secretion of hormones, which antagonize the action of insulin, is facilitated in response to surgery, and acute resistance to the action of insulin develops. Our aim is to elucidate the effects of intraoperati...
Citation: JA Clinical Reports 2018 4:9
Coagulation disorder and intraoperative hypotension are representative complications of traumatic brain injury which cause worse perioperative outcome. The aim of this study was to survey the relation of coagu...
Citation: JA Clinical Reports 2018 4:8
Goal-directed therapy (GDT) is beneficial for surgical patients, especially for those undergoing high-risk surgery. However, little has been reported on the hemodynamic effects of GDT in extensive surgery. We ...
Citation: JA Clinical Reports 2018 4:7
Spinal cord infarction (SCI) after epidural anesthesia is quite rare. Although most cases of perioperative SCI are associated with aortic, cardiac, or spinal surgery, and/or abnormal preoperative conditions, s...
Citation: JA Clinical Reports 2018 4:6
The Nihon Kohden linear inflationary non-invasive blood pressure (iNIBP) monitoring technology is an oscillometric device that measures blood pressure by detecting oscillations during inflation. Systolic blood...
Citation: JA Clinical Reports 2018 4:5
We describe a pediatric patient who suffered from critical abdominal distention caused by a combination of humidified, high-flow nasal cannula (HHFNC) oxygen therapy and nasal airway.
Citation: JA Clinical Reports 2018 4:4
Ovarian vein thrombosis is a rare complication of pregnancy. The representative complaints of patients with ovarian vein thrombosis are abdominal pain and fever. In some cases, however, fatal pulmonary embolis...
Citation: JA Clinical Reports 2018 4:3
Cleidocranial dysplasia is a type of skeletal dysplasia, which is primarily characterized by delayed ossification of skeletal structures. It causes facial and oral abnormalities, resulting in difficult airway ...
Citation: JA Clinical Reports 2018 4:2
Because there is ongoing population aging, the age of patients admitted to the intensive care unit (ICU) is also higher. However, the evidence about outcomes in elderly patients is insufficient in Japan. There...
Citation: JA Clinical Reports 2018 4:1
Citation: JA Clinical Reports 2017 3:67
Mediastinal tumor in a pregnant woman, which had needed a multidisciplinary approach, was further complicated by tuberculosis. The clinical course of the current patient was very complicated. A 37-year-old fem...
Citation: JA Clinical Reports 2017 3:66
It has been reported that PECS II block can alleviate postoperative pain following transapical transcatheter aortic valve implantation (TA-TAVI). However, the effectiveness of continuous PECS II block with cat...
Citation: JA Clinical Reports 2017 3:65
Becker muscular dystrophy (BMD) is a progressive neuromuscular disorder caused by mutations in the dystrophin gene. The sensitivity to non-depolarizing muscle relaxant in a patient with muscle dystrophy is rep...
Citation: JA Clinical Reports 2017 3:64
Coronary artery to pulmonary artery fistula is an unusual vascular anomaly, and the shunt ratio of this fistula is usually small.
Citation: JA Clinical Reports 2017 3:63
Tracheoesophageal fistulas (TEF) present a perioperative management challenge. A 62 year-old man with esophageal carcinoma presented with a large tracheoesophageal fistula extending most of the trachea. Previo...
Citation: JA Clinical Reports 2017 3:62
Thoracic outlet syndrome (TOS) can interrupt blood flow to upper limbs by vascular compression. We report a case of a 52-year-old man who presented left subclavian artery malperfusion due to TOS during total v...
Citation: JA Clinical Reports 2017 3:61
There has been an increase in the number of Japanese patients with lumbar spinal canal stenosis (LSCS) who complain of chronic pain or motor disturbance in the lower back or extremities. These patients are oft...
Citation: JA Clinical Reports 2017 3:60
Inclusion body myositis (IBM) is an inflammatory muscle disease characterized by slowly progressive muscle weakness and wasting, especially affecting proximal leg and distal arm. We report a successful anesthe...
Citation: JA Clinical Reports 2017 3:59
