Table 1 Case mix and surgical and anesthetic characteristics of patients with glycogen storage disease type Ia
Reference | Age, years (sex) | Surgery | Anesthetic | Type of infusion and glucose dosage | Others |
|---|---|---|---|---|---|
Cox JM (1968) [7] | 17 | Resection of chondromas of the femoral head | STP, S, Hal, N2O | B) G5 solution | Lactic acidosis |
Bevan JC. (1980) [8] | 9 (M) | Femoral osteotomy | STP, S, N2O, TC, Hal | A) G: 6.7Â mg/kg/min B) G17 solution C) G17 solution | N/A |
Bustamante SE, et al. (2006) [6] | 4 (F) | Tonsillectomy | Sev, F, Ro, Prop, RF, N2O | A) G5 solution and 0.45NS | Postoperative acute pancreatitis |
Oshita A, et al. (2008) [9] | 19 (M), 31 (F) | Liver segmentectomy | None reported | B) G: 3.3 mg/kg/min C) G: 6.6–9.8 mg/kg/min or G: 6.6 mg/kg/min + rapid-acting insulin 5 IU/h | Hypoglycemia, metabolic acidosis |
Takeuchi M, et al. (2010) [10] | 7 (F) | STA-MCA Bypass surgery | MZ, F, Ro, N2O, Sev | B) G5-7 solution | Lactic acidosis, decreased ventilation volume |
Mollet-Boudjemline A, et al. (2011) [11] | 34 (M) 23 (F) 24 (F) 26 (F) 20 (M) 18 (M) | Hepatectomy | None reported | A) G: 4 mg/kg/min + corticoid B) G: 6.0 mg/kg/min C) G: decreased by 1 mg/kg/min every 8 h | Lactic acidosis in 5 of 6 patients, hypoglycemia in 2 of them |
Mikuriya Y, et al. (2012) [12] | 39 (M) | Liver segmentectomy | None reported | B) G: 3.3 mg/kg/min C) G: 6.6–9.8 mg/kg/min or G: 6.6 mg/kg/min + rapid-acting insulin 5 IU/h | N/A |